FAH Monoclonal antibody, PBS Only

FAH Monoclonal Antibody for WB, IF/ICC, Indirect ELISA
Cat No. 67986-1-PBS
Clone No.2F8E11

Host / Isotype

Mouse / IgG1

Reactivity

human, mouse, rat, pig

Applications

WB, IF/ICC, Indirect ELISA

Fumarylacetoacetate hydrolase, FAA, EC:3.7.1.2, Beta-diketonase, 2F8E11

Formulation:  PBS Only
PBS and Azide
PBS Only
Conjugate:  Unconjugated
Size/Concentration: 

--/ -

Freight/Packing: --

Quantity
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Product Information

67986-1-PBS targets FAH in WB, IF/ICC, Indirect ELISA applications and shows reactivity with human, mouse, rat, pig samples.

Tested Reactivity human, mouse, rat, pig
Host / Isotype Mouse / IgG1
Class Monoclonal
Type Antibody
Immunogen FAH fusion protein Ag6704 Predict reactive species
Full Name fumarylacetoacetate hydrolase (fumarylacetoacetase)
Calculated Molecular Weight 46 kDa
Observed Molecular Weight 40-45 kDa
GenBank Accession NumberBC002527
Gene Symbol FAH
Gene ID (NCBI) 2184
RRIDAB_2918735
Conjugate Unconjugated
Form Liquid
Purification MethodProtein A purification
UNIPROT IDP16930
Storage Buffer PBS Only
Storage ConditionsStore at -80°C.

Background Information

FAH is also named as FAA(fumarylacetoacetase), the last enzyme in tyrosine degradation, functionally important in the liver and kidney(PMID:8473520). FAH is a metabolic enzyme catalyzing the last step of tyrosine and phenylalanine catabolism: the hydrolysis of fumarylacetoacetate into acetoacetate and fumarate. In humans, deficiency of this activity is associated with the metabolic disease hereditary tyrosinaemia type I, which is also known as hepatorenal tyrosinaemia(PMID:17768357).

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